apical hypertrophic cardiomyopathy

apical hypertrophic cardiomyopathy

An uncommon variant of hypertrophic cardiomyopathy (HCM), which is characterised by myocardial hypertrophy, predominantly in the left ventricular apex, which constitutes up to 25% of all HCM in Japan, but less than 5% of non-Japanese populations.
Associations, apical HCM Sudden cardiac death, severe arrhythmias, and apical infarctions with apical aneurysms, imparting a “spade-shaped” configuration of the LV cavity at end-diastole on ventriculography and “giant” T-wave negativity in the EKG.
Diagnosis Echocardiography, cardiac MRI should be performed if EKG raises suspicion of apical HCM.