histidine ammonia-lyase


his·ti·dine am·mo·ni·a-ly·ase

an enzyme catalyzing deamination of l-histidine to urocanate and ammonia; this enzyme is absent or deficient in people with histidinemia. Synonym(s): histidase, histidinase, histidine deaminase

his·ti·dine am·mo·ni·a-ly·ase

(his'ti-dēn ă-mō'nē-ă-lī'ās) An enzyme catalyzing deamination of l-histidine; this enzyme is absent or deficient in people with histidinemia.
Synonym(s): histidase.

histidine ammonia-lyase

A liver enzyme that catalyzes l-histidine with the resultant formation of urocanic acid and ammonia. Deficiency of this enzyme causes histidinemia. See also: histidine