Kasabach-Merritt syndrome


Kas·a·bach-Mer·ritt syn·drome

(kas'ă-bahk mer'it), thrombocytopenia and consumptive coagulopathy developing in a large hemangioma, usually in early infancy.

Kas·a·bach-Mer·ritt syn·drome

(kahs'ă-bok-mer'it sin'drōm) Large, bluish, progressive vascular malformations in extremities. Stagnation of blood in lesions can cause disseminated intravascular coagulation, platelet consumption, and bleeding. Condition usually affects infants; sudden growth of lesion causes depletion of platelets. Mortality rate is around 30%.

Kasabach,

Haig H., U.S. physician, 1898-1943. Kasabach-Merritt syndrome - capillary hemangioma associated with thrombocytopenic purpura. Synonym(s): hemangioma-thrombocytopenia syndrome

Merritt,

Katharine Krom, U.S. pediatrician, 1886–. Kasabach-Merritt syndrome - see under Kasabach