low-grade fibromyxoid sarcoma

low-grade fibromyxoid sarcoma

low-grade malignant tumor of soft tissues of proximal extremities or trunk, composed of fibroblasts forming myxoid areas or surrounding giant collagen rosettes. Synonym(s): fibromyxoid type fibrosarcoma, hyalinizing spindle cell tumor with giant rosettes

low-grade fibromyxoid sarcoma

A rare, deep soft-tissue sarcoma of young adults with a deceptively bland appearance, which is characterised by local recurrences and, eventually, metastases to lung and bone.
DiffDx Benign
Deep fibromatosis, nodular fasciitis.
DiffDx Malignant
Leiomyosarcoma, myofibrosarcoma, sclerosing epithelioid fibrosarcoma, low-grade fibrosarcoma, classic fibrosarcoma, inflammatory myxohyaline/myxoinflammatory fibroblastic sarcoma.
Prognosis
Local recurrence, 9%; metastases, 6%; death, 2%.