Arnold-Chiari malformation


Ar·nold-Chi·a·ri mal·for·ma·tion

(ar'nŏld kē-ah'rē), [MIM*207950] malformed posterior fossa structures associated with caudad traction and displacement of the rhombencephalon as caused by tethering of the spinal cord; may be accompanied in some cases by spina bifida and associated anomalies such as meningomyelocele; usually multifactorial in inheritance. Synonym(s): Arnold-Chiari deformity, Arnold-Chiari syndrome, cerebellomedullary malformation syndrome

Arnold-Chiari malformation

A congenital compression deformity of the lower brain, which is characterised by herniation of the cerebellar tonsils and distal medulla oblongata through the foramen magnum into the spinal canal. The Arnold-Chiari malformation is accompanied by compression of the 4th ventricle and firm adhesions at the cisterna magna.

Arnold-Chiari malformation

Neurology A congenital compression deformity of the 'lower brain' characterized by herniation of the cerebellar tonsils and distal medulla oblongata through the foramen magnum into the spinal canal; ACM is accompanied by compression of the 4th ventricle and firm adhesions at the cisterna magna

Ar·nold-Chi·a·ri mal·for·ma·tion

(ahr'nŏld kē-ah'rē mal'fōr-mā'shŭn) Deformity of posterior cranial fossa structures caused by tethering of the spinal cord with caudad traction and displacement of the rhombencephalon; may be accompanied by spina bifida and associated anomalies such as meningomyelocele; weak evidence of autosomal recessive inheritance.

Arnold,

Julius, German pathologist, 1835-1915. Arnold bodies - small portions or minute fragments of erythrocytes.Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformationArnold-Chiari malformation - malformed posterior fossa structures. Synonym(s): Arnold-Chiari deformity; Arnold-Chiari syndrome; cerebellomedullary malformation syndromeArnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformation

Chiari,

Hans, German pathologist, 1851-1916. Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformationArnold-Chiari malformation - see under Arnold, JuliusArnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformationBudd-Chiari syndrome - Synonym(s): Chiari syndromeChiari disease - Synonym(s): Chiari syndromeChiari net - abnormal fibrous or lacelike strands in the right atrium.Chiari syndrome - thrombosis of the hepatic vein with great enlargement of the liver and extensive development of collateral vessels, intractable ascites, and severe portal hypertension. Synonym(s): Budd-Chiari syndrome; Budd syndrome; Chiari-Budd syndrome; Chiari disease; Rokitansky disease (2)Chiari-Budd syndrome - Synonym(s): Chiari syndromeChiari II syndrome - elongation of medulla and cerebellar tonsils and vermis with displacement through the foramen magnum into the upper spinal canal.