macular dystrophy


mac·u·lar ret·i·nal dys·tro·phy

(mak'yū-lahr ret'i-năl dis'trŏ-fē) A group of disorders predominantly involving the posterior portion of the ocular fundus, due to degeneration in the sensory layer of the retina, retinal pigment epithelium, Bruch membrane, choroid, or a combination of these tissues.
See: Stargardt disease, Best disease
Synonym(s): macular dystrophy.

macular dystrophy

Any inherited, progressive degeneration of the macula lutea retinae marked by progressive central visual loss beginning in childhood or adolescence. Representative forms of macular dystrophy include Best disease and Stargardt disease. See: macula lutea retinaeSee also: dystrophy