main en griffe


main

 [mă] (Fr.) hand.main en griffe [man-ong-grēf´] clawhand.
The hand deformity characterised by flexion and atrophy, which may follow the claw foot deformity of Charcot-Marie-Tooth disease, in which the atrophy is usually confined to the distal arm; clawhand deformity may also occur in Dejerine-Sottas’ hypertrophic polyneuropathy, leprosy, and Refsum’s disease; a similar ‘stiff hand’ occurs in mucopolysaccharidosis, type I-S