systemic vasculitis

systemic vasculitis

Noninfectious vasculitis Vascular disease Any of a number of conditions characterized by inflammation of vessels in multiple sites in the body, which share many clinical and lab features Clinical Fever, fatigue, anorexia, weight loss, polymyalgia rheumatica, nondestructive oligoarthritis Lab ↑ ESR, anemia, thrombocytosis, ↓ albumin Pathogenesis Unknown Management Corticosteroids, cytotoxic agents; the various forms of SV have been formally classified by the Chapel Hill Consensus Conference according to size–small, medium-sized, large, and the major forms defined. See Vasculitis. Systemic vasculitis
Large vessel vasculitis
Giant cell (temporal) arteritis  Takayasu's arteritis Medium-sized vessel vasculitis
Polyarteritis nodosa  Kawasaki's disease  Primary granulomatous CNS vasculitis Small vessel vasculitis
ANCA-associated small vessel vasculitis  Churg-Strauss syndrome  Drug-induced ANCA-associated vasculitis  Microscopic polyangiitis  Wegener's granulomatosis  Immune complex small vessel vasculitis  Behçet's disease  Cryoglobulinemic vasculitis  Drug-induced immune complex vasculitis  Goodpasture syndrome  Henoch-Schönlein purpura  Hypocomplementemic urticarial vasculitis  Infection-induced immune complex vasculitis  Lupus vasculitis  Rheumatoid vasculitis  Serum sickness vasculitis  Sjögren syndrome vasculitis  Paraneoplastic small vessel vasculitis Carcinoma-induced vasculitis Lymphoproliferative neoplasm-induced vasculitis Myeloproliferative neoplasm-induced vasculitis  Inflammatory bowel disease vasculitis