Strumpell-Marie disease


spondylitis

 [spon″dĭ-li´tis] inflammation of the vertebrae, usually a serious and chronic disorder. It may be associated with tuberculosis of the bones, in which case it is called pott's disease. The vertebrae become eroded and collapse, causing kyphosis. Spondylitis may also be associated with other infectious diseases, such as brucellosis, in which the intervertebral disks and the vertebrae are affected and sometimes destroyed; this is one cause of spondylitis" >ankylosing spondylitis, a particularly serious variety.ankylosing spondylitis (Bekhterev's spondylitis) a form of arthritis" >rheumatoid arthritis that affects the spine, characterized by inflammation of the facet joints and inflammatory changes of the stabilizing ligaments of the spine (enthesopathy). It affects males almost exclusively. There is stiffening of spinal joints and ligaments, so that movement becomes increasingly painful and difficult. When it runs its full course, it results in bony ankylosis of the vertebral joints, which may extend to the ribs and limit the flexibility of the rib cage, so that breathing is impaired. Called also Marie-Strümpell disease or spondylitis and rheumatoid spondylitis.Typical posture of patient with ankylosing spondylitis. From Copstead and Banasik, 2000.Kümmell's spondylitis Kümmell's disease.Marie-Strümpell spondylitis ankylosing spondylitis.post-traumatic spondylitis Kümmell's disease.rheumatoid spondylitis ankylosing spondylitis.

an·ky·los·ing spon·dy·li·tis

[MIM*106300] arthritis of the spine, resembling rheumatoid arthritis, which may progress to bony ankylosis with ossification of the anterior and posterior longitudinal ligaments; the disease is more common in males, often with the rheumatoid factor absent and the HLA antigen present. There is a striking association with the B27 tissue type and the strong familial aggregation suggests an important genetic factor, perhaps inherited as an autosomal dominant [MIM*106300]; the mechanism, however, remains obscure. Synonym(s): Marie-Strümpell disease, rheumatoid spondylitis, Strümpell-Marie disease

Marie,

Pierre, French neurologist, 1853-1940. Bamberger-Marie disease - Synonym(s): Bamberger-Marie syndromeBamberger-Marie syndrome - see under Bamberger, EugenBrissaud-Marie syndrome - see under BrissaudCharcot-Marie-Tooth disease - see under CharcotDebré-Marie syndrome - see under DebréFoix-Cavany-Marie syndrome - see under FoixMarie ataxia - obsolete term for a variety of non-Friedreich hereditary ataxias.Marie-Leri syndrome - swelling of deformed joints.Marie-Sainton syndrome - excessive head development. Synonym(s): cleidocranial dysplasia; cleidocranial dysostosisMarie-Strümpell disease - Synonym(s): Strümpell-Marie diseaseMarie I syndrome - Synonym(s): Menzel syndromeMarie II syndrome - endocrine and neurologic disorders.Nonne-Marie syndrome - Synonym(s): Menzel syndromeStrümpell-Marie disease - see under Strümpell

Strümpell,

Ernst Adolf von, German physician, 1853-1925. Fleischer-Strümpell ring - Synonym(s): Kayser-Fleischer ringMarie-Strümpell disease - Synonym(s): Strümpell-Marie diseaseStrümpell disease - arthritis and osteitis deformans involving the spinal column. Synonym(s): acute epidemic leukoencephalitis; spondylitis deformansStrümpell-Marie disease - arthritis of the spine, resembling rheumatoid arthritis, that may progress to bony ankylosis. Synonym(s): ankylosing spondylitis; Marie-Strümpell diseaseStrümpell phenomenon - dorsal flexion of the great toe in a paralyzed limb when the limb is drawn up against the body, flexing knee and hip. Synonym(s): tibial phenomenonStrümpell reflex - stroking the abdomen or thigh causes flexion of the leg and adduction of the foot.Strümpell-Westphal disease - Synonym(s): Wilson diseaseWestphal-Strümpell pseudosclerosis - Synonym(s): Wilson disease