Spaghetti Tumour
Management Cytoreductive surgery, i.e., bilateral annexectomy and total hysterectomy; medical management with adjuvant progestin therapy is currently the most effective treatment for curing and preventing local recurrence. Aromatase inhibitors may be effective
Behaviour Local recurrence occurs in 70% of cases; metastasis is rare even after suboptimal surgical excision
Prognosis ± 85% 15-year survival, despite metastases