释义 |
scimitar sign scim·i·tar signa curvilinear structure seen radiographically in the lung and associated with anomalous pulmonary venous drainage, suggesting the sickle shape of a saber; also used to refer to the scalloped shape of the sacrum in spinal dysraphism with anterior meningocele.A rare vascular anomaly which is more common in females that may present in early childhood, in which some or all of the pulmonary veins drain into the inferior vena cava. The scimitar syndrome is often accompanied by hypoplasia of the right lung (RL), dextrocardia, and systemic arterial supply to the RL from descending aorta Surgical anatomy RL and right pulmonary artery hypoplasia, dextrocardia, anomalous origin of pulmonary arteries from the aorta to RL, anomalous venous drainage of RL into the inferior vena cava and anomalous right diaphragm Management Pneumonectomy or correction of cardiovascular ‘plumbing’ defects.scim·i·tar sign (si'mi-tahr sīn) A curvilinear structure seen in the lung roentgenographically, associated with anomalous pulmonary venous drainage, suggesting the sickle shape of a Turkish saber; also used to refer to the scalloped shape of the sacrum in spinal dysraphism with anterior meningocele. |