encephalotrigeminal angiomatosis

Sturge-Web·er syn·drome

(stŭrj vā'bĕr), [MIM*185300] in its complete form, a triad of unilateral occurrence of congenital capillary malformation (flame nevus) in the distribution of the trigeminal nerve; ipsilateral leptomeningeal vascular malformations with intracranial calcification and neurologic signs; and vascular malformation of the choroid plexus, often with secondary glaucoma. Inheritance is unclear with most cases sporadic.
See also: encephalotrigeminal vascular syndrome, Jahnke syndrome.
Synonym(s): cephalotrigeminal angiomatosis, encephalotrigeminal angiomatosis, Sturge-Kalischer-Weber syndrome, Sturge-Weber disease

Sturge-Web·er syn·drome

(stŭrj vā'bĕr), [MIM*185300] in its complete form, a triad of unilateral occurrence of congenital capillary malformation (flame nevus) in the distribution of the trigeminal nerve; ipsilateral leptomeningeal vascular malformations with intracranial calcification and neurologic signs; and vascular malformation of the choroid plexus, often with secondary glaucoma. Inheritance is unclear with most cases sporadic.
See also: encephalotrigeminal vascular syndrome, Jahnke syndrome.
Synonym(s): cephalotrigeminal angiomatosis, encephalotrigeminal angiomatosis, Sturge-Kalischer-Weber syndrome, Sturge-Weber disease

Sturge,

William Allen, English physician, 1850-1919. Sturge syndromeSturge-Kalischer-Weber syndrome - Synonym(s): Sturge-Weber syndromeSturge-Weber disease - Synonym(s): Sturge-Weber syndromeSturge-Weber syndrome - a triad of (1) congenital flame nevus in the distribution of the trigeminal nerve, usually unilateral; - (2) homolateral meningeal angioma with intracranial calcification and neurologic signs; and - (3) angioma of the choroid, often with secondary glaucoma. Synonym(s): cephalotrigeminal angiomatosis; encephalotrigeminal angiomatosis; Sturge-Kalischer-Weber syndrome; Sturge-Weber disease