debrancher deficiency

branch·er gly·co·gen stor·age dis·ease

type of glycogen storage disease, due to deficiency of amylo-1,4-1,6-transglucosidase (brancher enzyme). Synonym(s): brancher deficiency glycogenosis, debrancher deficiency, glycogenosis type 4

debrancher deficiency

Glycogen storage disease III, see there.