Congenital Giant Nevus

Also commonly called Bathing Trunk Nevus. A premalignant congenital melanocytic nevus, which measures > 5 cm in greatest dimension and has a ‘garment-like’ distribution—bathing trunk, cap, coat sleeve, stocking—often with scattered satellite lesions; up to 12% develop melanoma; GNs may be 20 cm in greatest dimension with satellite lesions, deeply pigmented with moderate hair growth, require multiple excisions; head & neck and leptomeningeal involvement may be associated with epilepsy, mental retardation, leptomeningeal melanoma; draining lymph nodes are often pigmented, corresponding to benign nevus cell aggregates