congenital hypogammaglobulinemia


congenital hypogammaglobulinemia

(1) Familial hypogammaglobulinemia, OMIM:240500. 
(2) Congenital agammaglobulinaemia(s), see there.

congenital hypogammaglobulinemia

Total immunoglobulin levels that are below 250 mg/dl. Chronic bacterial infections are common. Administration of intravenous immune globulin (beginning at 200 mg/kg per month) is usually effective. See also: hypogammaglobulinemia