Recognition of the absence of this murmur can indicate a potentially terminal cardiac defect in the newborn.

Cardiac defects are amongst the most common birth defects.

Cor triatriatum represents 0.1% of all congenital cardiac malformations and may be associated with other cardiac defects in as many as 50% of cases.

Cardiac defects include ventral and atrial septation and problems with the conduction system.

Symptoms such as syndactyly, cleft palate, short stature, and cardiac defects are seen more commonly in individuals with the autosomal recessive form of the disorder.