erythrokeratodermia

erythrokeratodermia

 [ĕ-rith″ro-ker″ah-to-der´-me-ah] reddening and hyperkeratosis of the skin.erythrokeratodermia varia´bilis a rare, dominantly inherited ichthyosis characterized by circumscribed areas of erythema that undergo changes in size, shape, and distribution over a period of days, with plaques of yellow-brown scales that occur in the areas of erythema. The usual onset is at birth or in the first year of life, and the disease runs a chronic course with remissions and exacerbations.

e·ryth·ro·ker·a·to·der·mi·a

(ĕ-rith'rō-ker-ă-tō-der'mē-ă), [MIM*133190] A neurocutaneous syndrome characterized by papulosquamous erythematous plaques with onset shortly after birth; ataxia, nystagmus, dysarthria, and decreased tendon reflexes appear later in life; symmetric progressive erythrokeratodermia is inherited as an autosomal dominant disorder and does not involve the palms and soles. [erythro- + G. keras, horn, + derma, skin, + -ia, condition]

e·ryth·ro·ker·a·to·der·mi·a

(ĕ-rith'rō-ker-ă-tō-dĕr'mē-ă) A neurocutaneous syndrome characterized by papulosquamous erythematous plaques with onset shortly after birth; ataxia, nystagmus, dysarthria, and decreased tendon reflexes appear later in life; symmetric progressive erythrokeratodermia is inherited as an autosomal dominant disorder and does not involve the palms and soles. [erythro- + G. keras, horn, + derma, skin, + -ia, condition]