释义 |
DictionarySeeVon Gierke diseaseGierke, Edgar von
Gierke, Edgar von, German pathologist, 1877-1945. Fibiger-Debré-von Gierke syndrome - Synonym(s): Debré-Fibiger syndromeGierke disease - glycogenosis due to glucose 6-phosphatase deficiency, resulting in accumulation of excessive amounts of glycogen of normal chemical structure, particularly in liver and kidney. Synonym(s): type 1 glycogenosis; von Gierke disease; von Gierke syndromevon Gierke disease - Synonym(s): Gierke diseasevon Gierke syndrome - Synonym(s): Gierke disease |