crystal-storing histiocytosis
crystal-storing histiocytosis
A rare complication of low-grade B cell lymphoma and monoclonal gammopathies, including myelomas, which is characterised by lysosomal storage of kappa light chain (KLC) crystals.Clinical findings
It may be associated with adult Fanconi syndrome, chronic tubulo-interstitial nephritis with accumulation of monoclonal KLC crystals within proximal tubular cell.
DiffDx
Benign rhabdomyoma.